HIP ABNORMALITIES IN CHILDREN WITH CHARCOT-MARIE-TOOTH DISEASE

Hip dysplasia was recently observed in association with Charcot-Marie- Tooth disease (CMT). We retrospectively reviewed available radiographs of 74 of 100 children with clinically and electrodiagnostically prove n CMT and noted six cases of hip dysplasia. Minor hip abnormalities, m ost commonly increased neck shaft angles, were noted in 21 other patie nts. Type I usually causes more weakness and had more hip dysplasia th an type II. A female predominance was noted but may have resulted from sampling of more immature radiographs in males. Most dysplasia was as ymptomatic and was detected only on screening radiographs.