INTRASELLAR PARAGANGLIOMA - REPORT OF A CASE IN A SIBSHIP OF VON HIPPEL-LINDAU DISEASE

ALTHOUGH UNCOMMON, PARAGANGLIOMAS are known to affect the central nerv ous system. Those that arise in the sellar region are particularly rar e. We report the clinicopathological features of a paraganglioma occur ring in the setting of von Hippel-Lindau disease, a disorder in which paragangliomas are known to occur. We also present a review of the lit erature.