An ectopic, nonsecreting chromaffin tumour was revealed by vena cava c
ompression responsible for pulmonary embolism. Based on radiological f
indings, the first hypothesis was a hepatic cystic tumour. The final d
iagnosis was confirmed by histological examination of the tumour. Ecto
pic sites of adrenal tumours and their embryology, diagnosis and thera
peutic problems are discussed in the light of this case.