A histologically unique glioneuronal neoplasm occupying the lateral ve
ntricle of a child was immunohistochemically and ultrastructurally cha
racterized. Its principal component exhibited the characteristic featu
res of ependymoma, whereas a minor population of neuroendocrine cells,
occurring singly and in small clusters, lay scattered throughout the
ependymoma component. Yet another unusual finding was the presence of
numerous elastic fibers within the extracellular matrix. This tumor is
considered to represent a true mixed neoplasm consisting of ependymal
and neuroendocrine elements.