Cystic dystrophy of the aberrant pancreas is a rare poorly understood
condition which is difficult to diagnose and treat. The primary clinic
al signs are epigastralgia associated with poor general health and com
plications due to stenosis of the duodenum. Endoscopy gives the most i
nformation on tissue lesions and cystic formations in rite duodenal mu
cosa. Although the condition is benign, and due to the lack of suffici
ent history in endoscopically treated cases, cystic dystrophy of the a
berrant duodenal pancreas appears to require duodenopancreatectomy.