RUPTURED HEPATIC ANGIOLIPOMA IN TUBEROUS SCLEROSIS COMPLEX

Tuberous sclerosis complex (TSC) may be associated with hepatic angiom yolipoma. In contradistinction to renal angiomyolipoma this lesion is rare, and nontraumatic hemorrhage has not so far been described. This is the first report of a spontaneously ruptured, surgically treated an d histologically verified, hepatic angiomyolipoma in TSC. Anomalies of the vessel walls and consequently the hazard of bleeding are known to increase with the diameter of the tumor in other localizations. It is concluded that in cases with rapid tumor growth and marked vessel ano malies elective surgery should be considered.