LARGE BILATERAL PULMONARY-ARTERY ANEURYSMS IN BEHCETS-DISEASE - RUPTURE OF THE CONTRALATERAL LESION AFTER ANEURYSMORRHAPHY

An 18-year-old man presented with Behcet's disease and two large bilat eral pulmonary artery aneurysms, The day following aneurysmorrhaphy of the right aneurysm, a massive hemoptysis led to death, Postmortem exa mination disclosed rupture of the left aneurysm in a segmental bronchu s, The aneurysms had inflammatory walls and were associated with organ ized pulmonary arterial thromboses and endomyocardial fibrosis of the right ventricle. Our case report highlights the surgical risk of ruptu re of associated arterial lesions, certainly related to per- and posto perative pulmonary arterial pressure variations.