We describe hepatic granulomata in a patient with familial granulomato
us synovitis (Blau syndrome). While visceral involvement is a previous
ly unrecognized manifestation of Blau syndrome, its occurrence has bee
n well documented in a similar disease, childhood sarcoidosis. Our fin
dings suggest that the 2 conditions (Blau syndrome and childhood sarco
idosis) are more closely related than thought.