MAJOR INTRAHEPATIC VENOVENOUS FISTULAS AFTER A MODIFIED FONTAN OPERATION

After the Fontan operation, systemic venous hypertension drives transp ulmonary blood now. Owing to this physiology, there is a significant i ncidence of effusions, splanchnic congestion, and generalized edema. T o attenuate the effusive problems, partial exclusion of the hepatic ve ins has been recently practiced by Jacobs and Norwood. This report con cerns a patient we recently treated for profound progressive cyanosis due to an acquired intrahepatic venovenous shunt after a Fontan operat ion with partial hepatic vein exclusion.