3-QUADRANT SYNDROME WITH KLIPPEL-TRENAUNA Y-SYNDROME COMBINED WITH CONGENITAL LYMPHEDEMA OF BOTH LEGS

A 34-year-old woman with extensive Klippel-Trenaunay syndrome is prese nted. Clinical and radiological tests demonstrated that three quadrant s are affected with haemangiomas, varicose veins and bone abnormalitie s. In addition, our patient suffers from congenital lymphoedema of bot h legs. Associated findings such as intestinal haemangiomata, vascular hamartomas, lipomas or ar-teriovenous abnormalities of the spinal cor d were not apparent. The treatment is only symptomatic with compressio n bandages and an orthopaedic appliance for compensation of the differ ent leg length.