Acinar cell carcinoma of the pancreas is a rare tumor of the exocrine
pancreas that may be associated with a characteristic syndrome of diss
eminated fat necrosis with a bad prognosis. We report a a case of this
tumor occurring ina 63 year-old man who presented with polyarthralgia
and panniculitis of the legs. The histological features and the diffe
rential diagnosis of acinar cell carcinoma are discussed.