We report a 4 year-old boy affected with hypohidrotic ectodermal dyspl
asia in whom loose anagen hair syndrome (LAHS) was suspected clinicall
y, The diagnosis was confirmed by examination of hair by optic and sca
nning electron microscopy. Loose anagen hairs have not been previously
described in the ectodermal dysplasias. It is possible that our patie
nt had real LAHS or an ectodermal dysplasia with loose anagen hair as
an epiphenomenon.