ANOMALIES IN THE PERMANENT DENTITION AND OTHER ORAL FINDINGS IN 29 INDIVIDUALS WITH LAURENCE-MOON-BARDET-BIEDL SYNDROME

This paper reports a clinical and roentgenological examination of the teeth, jaws and saliva of 29 Scandinavian individuals with Laurence-Mo on-Bardet-Biedl (LMBB) syndrome, whose cardinal signs are retinal dyst rophy. polydactyly, obesity, hypogenitalism and mental retardation. Al l subjects had at least three of these signs, including retinal dystro phy. Compared with normal subjects, the group had statistically signif icantly higher frequencies of hypodontia, small teeth and short roots. In addition, the saliva showed a buffering capacity higher than norma l. In conclusion, there seem to exist disturbances of both dental and skeletal formation in the LMBB syndrome.