A child with Morquio syndrome developed severe cervical kyphosis causi
ng myelopathy. Decompression of the spinal cord was accomplished by an
anterior approach using multilevel corpectomies and stabilization wit
h calvarial bone grafts and halo immobilization. The case reported is
unique in that cervical cord compression resulted from an uncommon deg
ree of cervical kyphosis rather than the usual at lantoaxial instabili
ty seen in patients with Morquio syndrome. The operative procedure des
cribed shows another example of the usefulness of calvarial bone graft
s for cervical spine fusions in children.