H. Dominguez et al., MULTIPLE PULMONARY CHONDROHAMARTOMAS IN TRACHEA, BRONCHI AND LUNG PARENCHYMA - REVIEW OF THE LITERATURE, Respiratory medicine, 90(2), 1996, pp. 111-114
Citations number
17
Categorie Soggetti
Cardiac & Cardiovascular System","Respiratory System
Multiple pulmonary chondromatous hamartomas (MPCH) are rare, and MPCH
with tracheal involvement have not been, to the best of our knowledge,
reported before. Furthermore, there is no agreement in the literature
about the origin of these tumours. We report a case of MPCH involving
trachea, bronchi and lung parenchyma, incidentally found at the autop
sy of a 88-year-old woman who died of acute myocardial infarction, and
we review the literature about MPCH. We conclude that there appear to
be two different types of multiple pulmonary chondromatous hamartomas
; those presented in young patients often linked to gastric leiomyobla
stomas and catecholamine-producing paragangliomas (Carney syndrome) wi
th high mortality, and those presented in elderly patients, which seem
s to be compatible with life.