MYOCARDIAL-ISCHEMIA ASSOCIATED WITH EHLERS-DANLOS SYNDROME

A 38-yr-old man with an unusual type of Ehlers-Danlos syndrome present ed for elective abdominal aortic aneurysm repair. During surgery he de veloped acute myocardial ischaemia, resulting in abandonment of the pr ocedure. He was shown subsequently to have severe triple vessel corona ry artery disease. Silent ischaemia associated with severe coronary ar tery disease, although rare, may be associated with the syndrome and i s difficult to recognize as other cardiac abnormalities are frequently present.