A CASE-REPORT ABOUT HEMOGLOBIN SD DISEASE

A 7 year old Kurdish girl presented with a cerebral infarction and a r esulting hemiparesis following a blood transfusion. Examination of the blood film suggested sickle cell anaemia. However a simultaneously ca rried out haemoglobin electrophoresis showed haemoglobin S and haemogl obin D. The diagnosis of haemoglobin SD disease was thereby establishe d. This kind of haemoglobin disorder usually shows a mild clinical man ifestation. According to our knowledge such serious cases have not bee n published before. With this disease the main emphasis is on the prev ention of recurrent cerebral infarctions bay a long-term transfusion p rogramme whereas the effects of the cerebral infarction are treated in the usual way.