S. Nagahiro et al., MULTIPLE CEREBRAL ARTERIAL OCCLUSIONS IN A YOUNG PATIENT WITH SJOGRENS-SYNDROME - CASE-REPORT, Neurosurgery, 38(3), 1996, pp. 592-595
WE DESCRIBE A case of a young patient with multiple occlusions of majo
r cerebral arteries and Sjogren's syndrome. This 17-year-old female pa
tient experienced repeated transient ischemic attacks of right hemipar
esis, speech disturbance, and unconsciousness. Angiography revealed pr
ogressive occlusion of the bilateral carotid and vertebral arteries. E
xaminations, including a serological test, a rose bengal test, Ga scin
tigraphy, and a biopsy of the parotid gland, indicated Sjogren's syndr
ome. The patient was successfully managed with bypass surgery. Patient
s with Sjogren's syndrome may experience progressive occlusion of the
major cerebral arteries resembling that of moyamoya disease.