Extraskeletal mesenchymal chondrosarcoma is a rare tumor. It has been
noted to occur most commonly in muscle and the central nervous system.
It has never been reported to occur in the soft tissues of the anogen
ital region, We report the first such case, occurring in a 40-year-old
woman who presented with a 1-year history of a mass originating in th
e left labium majus. After extensive local resection and lymph node di
ssection she remains disease free after 40 months follow-up. (C) 1996
Academic Press, Inc.