EPIDERMOLYSIS-BULLOSA LETALIS WITH PYLORIC ATRESIA IN AN INFANT

Epidermolysis bullosa (EB) is a group of inherited diseases that are c haracterized by vesiculobullous lesions that arise in response to mini mal trauma or friction. The three major groups of EB differ according to the ultrastructural level of cleavage namely: simplex (epidermolyti c),junctional and dystrophic (dermolytic). The combination of EB and p yloric atresia is rare and there is a definite association between the m. We report a baby boy who died from epidermolysis bullosa complicati ons despite successful surgical correction of his pyloric atresia.