SIMULTANEOUS BILATERAL PALLIDOANSOTOMY FOR IDIOPATHIC DYSTONIA MUSCULORUM DEFORMANS

A 17-year-old Russian male with a 9-year diagnosed history of dystonia musculorum deformans manifested as severe tortipelvis, lordosis, and axial and appendicular spastic dystonia, refractory to medical therapy , is reported, This patient underwent a simultaneous bilateral pallido ansotomy with dramatic results, Postoperative evaluation revealed sust ained alleviation of all dystonic symptoms and abnormal movements, Rap id recovery of useful strength in all limbs as well as dramatic improv ement in coordination occurred, Bilateral posteroventral pallidotomy a nd pallidoansotomy in the past have proven effective in alleviation of all parkinsonian symptoms, including dyskinesia and dystonia, without the concurrent risk of intransigent side effects associated with bila teral thalamotomy or other stereotactic surgical procedures, Pallidoan sotomy may prove to be the treatment of choice for idiopathic torsion dystonia and merits further investigation.