SJOGRENS-SYNDROME PLASMA-CELL PANNICULITIS AND HIDRADENITIS

We present a 42-year-old woman with primary Sjogren's syndrome and a p olyclonal gammopathy who presented with pretibial petechiae, purpura, and tender indurated plaques. The indurated plaques revealed a lobular plasma cell panniculitis, and thus Sjogren's syndrome should be added to the short list of collagen vascular diseases that can present as p lasma cell panniculitis. Her biopsies also demonstrated intense periec crine plasma cell infiltrates that may account for Sjogren's syndrome- associated hypohidrosis. We also observed occasional vascular occlusio n of vessels with an amorphous, eosinophilic material possibly related to her hypergammaglobulinemic purpura.