PRIMARY ANTIPHOSPHOLIPID SYNDROME-ASSOCIATED WITH MESENTERIC INFLAMMATORY VENOOCCLUSIVE DISEASE

We describe a 24-year old Caucasian man with gangrene of small bowels and intestinal resection due to mesenteric inflammatory veno-occlusive disease (MIVOD) who later developed deep vein thrombosis in his left leg. He had no clinical evidence of an underlying symptomatic connecti ve tissue disease or Behcet's disease. An IgG anticardiolipin antibody titre above 60 GPL unit/mL and thrombocytopenia confirmed the diagnos is of primary antiphospholipid syndrome (APS). This is the first known case of APS associated with MNOD.