Childhood sarcoidosis is a rare disease with multisystemic organ invol
vement. A wide spectrum of vasculitides, including large vessel involv
ement, have been reported in childhood sarcoidosis. We describe a 7-ye
ar-old boy with childhood sarcoidosis who presented with prolonged fev
er, iritis, and abdominal aortic aneurysm. He underwent successful sur
gical repair of the abdominal aortic aneurysm and followup for 12 mont
hs was uneventful. This is the first report of abdominal aortic aneury
sm complicating childhood sarcoidosis.