A 15-year-old Japanese girl complained of decreased visual acuity in t
he left eye of 1-month duration. Histiocytosis X had been diagnosed wh
en she was 2 years old based on examination of biopsies of skin and ce
rvical lymph nodes and bone marrow aspirations. She had been in comple
te remission for 7 years. She exhibited the characteristic ophthalmosc
opic, ultrasonographic, and radiologic features of bilateral choroidal
osteomas.