The objective of this article was to offer a better characterization o
f the typical clinical presentation, radiologic findings, histology, t
reatment approaches, and differential diagnosis of cystic angiomatosis
, a rare condition of which previous reports have been confusing becau
se of unclear diagnostic criteria, different classifications, and vari
ations in terminology. A case report using the improved imaging techni
ques of computed tomography scanning is presented in addition to an an
alysis and review of the previous literature, which relied heavily on
plain film radiography, biopsy, and necropsy for diagnosis, A case rep
ort of a 26-year-old man initially symptomatic at age 12 is presented.
Although a rare condition, cystic angiomatosis must be considered in
pediatric and young adult patients presenting with diffuse, multifocal
. cystic skeletal lesions, with or without visceral involvement.