ROSAI-DORFMAN DISEASE PRESENTING WITH MULTIPLE ORBITAL AND INTRACRANIAL MASSES

Citation
Dk. Resnick et al., ROSAI-DORFMAN DISEASE PRESENTING WITH MULTIPLE ORBITAL AND INTRACRANIAL MASSES, Acta Neuropathologica, 91(5), 1996, pp. 554-557
Citations number
15
Categorie Soggetti
Neurosciences,"Clinical Neurology",Pathology
Journal title
ISSN journal
00016322
Volume
91
Issue
5
Year of publication
1996
Pages
554 - 557
Database
ISI
SICI code
0001-6322(1996)91:5<554:RDPWMO>2.0.ZU;2-A
Abstract
Rosai-Dorfman disease is an idiopathic histocytic proliferative disord er typically characterized by painless cervical adenopathy, fever, and weight loss. Extranodal manifestations are responsible for presentati on in approximately 25% of patients. Orbital involvement has been desc ribed in about 10% of patients, There have been only 16 reported cases of Rosai-Dorfman disease presenting with an intracranial mass. We rep ort an unusual case of a patient presenting with bilateral orbital tum ors as well as multiple intracranial masses. Clinical, magnetic resona nce imaging, and histopathological features are discussed.