Rosai-Dorfman disease is an idiopathic histocytic proliferative disord
er typically characterized by painless cervical adenopathy, fever, and
weight loss. Extranodal manifestations are responsible for presentati
on in approximately 25% of patients. Orbital involvement has been desc
ribed in about 10% of patients, There have been only 16 reported cases
of Rosai-Dorfman disease presenting with an intracranial mass. We rep
ort an unusual case of a patient presenting with bilateral orbital tum
ors as well as multiple intracranial masses. Clinical, magnetic resona
nce imaging, and histopathological features are discussed.