LINEAR DISRUPTION OF UMBILICAL-CORD - A RARE ANOMALY OF THE CORD ASSOCIATED WITH ACUTE FETAL DISTRESS AND PERINATAL DEATH PROFOUND PSYCHOMOTOR RETARDATION

We report on a non-malformed child with severe microcephaly and profou nd psychomotor delay. Review of the delivery/birth records documented descriptions consistent with linear disruption of the umbilical cord, This rare anomaly typically leads to acute fetal distress and perinata l death, Severe microcephaly and psychomotor delay without other anoma lies should prompt a careful review of the delivery/birth records to s earch for umbilical cord descriptions consistent with this diagnosis. (C) 1996 Wiley-Liss, Inc.