An ultrasonography scan detected a left upper quadrant abdominal mass
in a fetus of 20 weeks gestation. The mass was confirmed by a postnata
l ultrasonography scan, computerized tomography and magnetic resonance
imaging prior to surgery The sonographic characteristic of this lesio
n was that of a homogenous echogenic mass embedded in the left diaphra
gmatic crus: which moved with respiration. Histopathological evaluatio
n of the mass demonstrated alveolar and bronchial tissue, with its own
visceral pleural covering corroborating the diagnosis of extra-lobar
intra-abdominal pulmonary sequestration. Surgical excision is a valid
recommendation because of the uncertainty of preoperative diagnosis of
this uncommon malformation.