This report deals with a rare case of malignant fibrous histiocytoma i
n the left kidney of a 69-year-old male patient. Up to now, 21 cases o
f this tumour have been described in the worldwide literature. As comp
uterized axial tomography shows cystic and solid structures, benign cy
sts and renal cell carcinoma must be ruled out. The therapy of choice
consists of nephrectomy.