A UNIQUE TEMPORAL BONE LESION RESEMBLING JUVENILE ACTIVE OSSIFYING MYXOMA

Juvenile active ossifying fibroma (JAOF) is a lesion characterized by early age of onset, slow growth, frequent recurrence, and locally aggr essive behavior. Histologically, it consists of three major components : cellular fibrous stroma, osteoid bodies, and myxomatous matrix, whic h may become cystic. This article describes a case of a slowly growing destructive lesion of the mastoid in a 2-year-old girl with histologi c features resembling those of juvenile active ossifying myxoma (JAOM) . Histologically, its prominent features were myxoid and fibromyxoid s troma with cystic areas, vascular spaces, bone, and multinucleated gia nt cells. This is the first pediatric temporal bone lesion with these features recorded. These histologic components led to the diagnosis of JAOM of the temporal bone, probably developing in relation to the dev elopment of the mastoid air spaces.