Cockayne syndrome is a rare autosomal recessive producing a dwarfed, m
entally retarded infant or child. Problems with airway management and
an increased risk of gastric aspiration are the main anaesthetic conce
rns. Anaesthetics given to three patients with Cockayne syndrome are d
escribed. In two of these, tracheal intubation was difficult and the u
se of a laryngeal mask airway proved invaluable.