CHRONIC HEPATITIS WITH CHRONIC MUCOCUTANE OUS CANDIDIASIS AND ECTODERMAL DYSTROPHY - REPORT OF A CASE

Authors
ROQUELAURE B MICHEL G GARNIER JM PIERRON H SARLES J
Citation
B. Roquelaure et al., CHRONIC HEPATITIS WITH CHRONIC MUCOCUTANE OUS CANDIDIASIS AND ECTODERMAL DYSTROPHY - REPORT OF A CASE, Annales de pediatrie, 43(3), 1996, pp. 239-243
Citations number
21
Categorie Soggetti
Pediatrics
Journal title
Annales de pediatrie → ACNP
ISSN journal
00662097
Volume
43
Issue
3
Year of publication
1996
Pages
239 - 243
Database
ISI
SICI code
0066-2097(1996)43:3<239:CHWCMO>2.0.ZU;2-G
Abstract
An adolescent with a history of clinically silent hepatitis since one year of age developed chronic candidiasis and dental enamel dysplasia. He was given a diagnosis of Autoimmune PolyEndocrinopathy-Candidiasis -Ectodermal Dystrophy (APECED). The literature on APECED is reviewed. Hepatic involvement is exceedingly rare in this condition.