ACRAL PERSISTENT PAPULAR MUCINOSIS

Introduction. Acral persistent papular mucinosis is an uncommon skin d isease with characteristic mucin deposits in the medial layer of the d erma. In the Rongioletti and Rebora classification, this disease belon gs to the group of specific cutaneous mucinoses. Case report. A 14-yea r-old girl consulted for symmetrical papular lesions on the back of th e hand and wrists. The first manifestations had occurred at the age of 3 years. Laboratory tests were positive for antinuclear antibodies al 1/320. The histology and the clinical presentation led to the diagnos is of acral persistent papular mucinosis. Discussion. This case shows that manifestations of acral persistent papular mucinosis can occur ea rly in childhood. This disease may be a single clinical entity or an a ttenuated clinical expression of papular mucinosis. Clinical and labor atory observation were required for our patient.