CRANIODIAPHYSEAL DYSPLASIA - ANOTHER CAUSE OF DIFFICULT INTUBATION

A nine-year-old boy with craniodiaphyseal dysplasia (CDD) presented fo r mandibular reduction. Patients with CDD present problems to the anae sthetist, specifically difficulties with airway management and trachea l intubation. This child was managed using laryngeal mask airway (LMA) guided fibreoptic intubation. Spontaneous respiration was maintained throughout intubation, following which ventilation was controlled and anaesthesia was provided using nitrous oxide, isoflurane and fentanyl. The perioperative management is described.