A nine-year-old boy with craniodiaphyseal dysplasia (CDD) presented fo
r mandibular reduction. Patients with CDD present problems to the anae
sthetist, specifically difficulties with airway management and trachea
l intubation. This child was managed using laryngeal mask airway (LMA)
guided fibreoptic intubation. Spontaneous respiration was maintained
throughout intubation, following which ventilation was controlled and
anaesthesia was provided using nitrous oxide, isoflurane and fentanyl.
The perioperative management is described.