SYMPTOMATIC INTRASELLAR HEMANGIOBLASTOMA IN A CHILD TREATED WITH SUBTOTAL RESECTION AND ADJUVANT RADIOSURGERY - CASE-REPORT

The first documented case of a symptomatic intrasellar hemangioblastom a is described, occurring in an 11-year-old girl with stigmata of von Hippel-Lindau disease who presented with headaches, progressive bitemp oral hemianopsia, and adenohypophysial dysfunction. A subtotal resecti on of the lesion was achieved with two separate surgical procedures: a transsphenoidal approach and a subfrontal craniotomy. Subsequent grow th of residual tumor was treated with combined conventional radiothera py and stereotactic radiosurgery. Two years following completion of th ese adjuvant therapies, no residual tumor was evident on magnetic reso nance imaging. Previous experience with hemangioblastoma in this regio n, as well as the rationale for radiotherapy in the treatment of incom pletely resected lesions, is reviewed.