We report four patients with ''dropped head syndrome,'' a recently des
cribed nonprogressive myopathy characterized by severe neck extensor w
eakness. This relatively benign condition may be confused with more om
inous neuromuscular disorders that also present with prominent neck we
akness. We compared clinical and laboratory data from the patients wit
h dropped head syndrome with findings from patients with head drop cau
sed by other neuromuscular conditions. Patients with ''isolated neck e
xtensor myopathy,'' a term we prefer to ''dropped head syndrome,'' cou
ld be readily identified with electrophysiologic, radiographic, and hi
stologic studies.