A case of endometrial stromal sarcoma of the uterus with rhabdoid feat
ures, occurring in a 57 year old woman is reported. Electron microscop
y and immunohistochemistry revealed that the rhabdoid cells contained
intermediate filaments which were positive for vimentin, cytokeratin,
alpha-smooth muscle actin, and muscle specific actin, but not for myog
lobin and desmin. This indicated that the tumor in this case differed
somewhat from the three rhabdoid tumors and an endometrial stromal sar
coma with rhabdoid differentiation previously reported and that, there
fore, these tumors were heterogeneous.