INTRACRANIAL FIBROMUSCULAR DYSPLASIA IN A 5-YEAR-OLD CHILD

A 5-year-old girl presenting with acute middle cerebral artery stroke was diagnosed as having intracranial fibromuscular dysplasia by angiog raphic findings of focal changes in the proximal right middle cerebral artery and pathological dilatation of the right internal carotid arte ry at the base of the skull, as well as dissection of at least one of the middle cerebral artery branches and nonfilling of two or perhaps t hree remaining middle cerebral artery segmental branches. Her clinical condition improved after management of the increased intracranial pre ssure. She did not receive any medication after discharge and had virt ually no residual sequelae, Our case documents an unusual location and age of onset of a patient with fibromuscular dysplasia.