Forty-two cases of perineurioma have been reported in the literature.
This report adds the first intratemporal facial nerve perineurioma to
the literature and reviews the others, Unlike schwannoma and neurofibr
oma, the histological features of perineurioma demonstrate onion bulb-
like structures with a strong positive immunoreactivity for epithelial
membrane antigen. The clinical history of gradual facial nerve paresi
s was 15 years in this case presentation and the clinical diagnosis of
tumor was overlooked.