THE PAPILLON-LEFEVRE-SYNDROME (2 NEW CASE -REPORTS)

Authors
TURKI H HACHICHA M BOUDAYA S CHAARI H BENJEMAA B ABID A TRIKI A ZAHAF A
Citation
H. Turki et al., THE PAPILLON-LEFEVRE-SYNDROME (2 NEW CASE -REPORTS), Annales de pediatrie, 43(4), 1996, pp. 312-315
Citations number
12
Categorie Soggetti
Pediatrics
Journal title
Annales de pediatrie → ACNP
ISSN journal
00662097
Volume
43
Issue
4
Year of publication
1996
Pages
312 - 315
Database
ISI
SICI code
0066-2097(1996)43:4<312:TP(NC->2.0.ZU;2-Y
Abstract
Two cases of Papillon-Lefevre syndrome are reported. Both patients wer e girls whose parents were first-degree cousins. Ages were nine and 14 years. Papillon-Lefevre syndrome is characterized by Meleda-type palm oplantar keratoderma and severe lysis of the alveolar ridge with shedd ing of the permanent teeth. Emphasis is put on the severity of the den tal prognosis and on the efficacy of retionoids on the cutaneous and d ental lesions.