MOYAMOYA PHENOMENON AND DOWN-SYNDROME

We present a case of a six-year-old girl with Down Syndrom who develop ed recurrent ischemic strokes. Cerebral angiography demonstrated a sup raclinoid stenosis of the right internal artery, an occlusion of the l eft supraclinoid internal cerebral artery and dilated collateral vesse ls, consistent with Moyamoya disease. We emphasize the increased frequ ency of Moyamoya in patients with Down Syndrome and also the most impo rtant pathophysiologic, clinical and radiological findings of this dis ease.