An elderly, hypertensive white female presented with acute left-sided
facial pain and a left pupil-involved third nerve palsy. She had no hi
story of head trauma. The remainder of the ocular exam was normal and
there was no evidence of proptosis, conjunctival injection or chemosis
, or increased intraocular pressure. A computed tomographic scan of th
e head suggested an enlarged cavernous sinus on the left side. Cerebra
l angiography revealed a posterior draining carotid-cavernous fistula.
A spontaneous carotid-cavernous fistula should be considered in the d
ifferential diagnosis of any ocular motor palsy, and may present witho
ut external eye signs if the predominant venous drainage is posterior
rather than anterior through the superior ophthalmic vein.