Cases with cardiac hydatid cyst disease are uncommon, being approximat
ely 0.2-2% of all cases. Most cardiac hydatid cysts are located in the
interventricular septum or left ventricular wall. Pericardial locatio
n is very rare. We report on a 12 year old girl with pericardial hydat
id cyst disease who was otherwise asymptomatic, having no cardiac symp
tomatology. Unfortunately the course of her disease was fatal. This is
the first report of uncommon localized hydatid disease with a fatal o
utcome.