A CASE OF KABUKI MAKE-UP SYNDROME WITH EBV-LYMPHOMA( BURKITTS)

Kabuki make-up syndrome was first reported in 1981 and is characterize d by peculiar facies with Post natal growth deficiency and mental reta rdation. Since the first report, approximately 100 cases have been rep orted, but there have been no reports of tumor development. A case is reported of patient with Kabuki make-up syndrome who developed maligna nt lymphoma in his abdomen at the age of 3 years. The tumor was histol ogically diagnosed as Burkitt's lymphoma and Epstein-Barr virus was de tected by in situ hybridization.