Objective: To demonstrate the appropriate diagnosis and management of
perineal endometriosis. Method: Six patients with perineal endometrios
is were diagnosed according to their clinical symptoms and signs which
included cyclic perineal pain and a tender perineal mass coinciding w
ith the menstrual cycle. Diagnostic tools used included ultrasonograph
y, computerized tomography, fine needle aspiration cytology and laparo
scopy, Management comprised both surgical and medical treatment. Posto
perative follow-up was carried out at 3-monthly intervals. Results: Al
l six patients were cured following surgical excision of the endometri
oma. Conclusion: A detailed history, thorough pelvic examination and s
onographic investigation are essential in diagnosing perineal endometr
iosis. The role of other diagnostic tools remains controversial. Treat
ment of extrapelvic endometriosis includes surgical intervention and h
ormonal suppression. If hormonal suppression fails; surgical excision
of the perineal endometrioma should be carried out.