MULTIPLE ENDOCRINE NEOPLASIA TYPE-1 PRESENTING AS ROSACEA

Citation
Jd. Creamer et al., MULTIPLE ENDOCRINE NEOPLASIA TYPE-1 PRESENTING AS ROSACEA, Clinical and experimental dermatology, 21(2), 1996, pp. 170-171
Citations number
6
Categorie Soggetti
Dermatology & Venereal Diseases
ISSN journal
03076938
Volume
21
Issue
2
Year of publication
1996
Pages
170 - 171
Database
ISI
SICI code
0307-6938(1996)21:2<170:MENTPA>2.0.ZU;2-9
Abstract
We present a case of malignant carcinoid initially diagnosed as rosace a. This patient was later found to have an additional functioning para thyroid tumour. Although a pituitary tumour was not identified, the as sociation represents a probable case of multiple endocrine neoplasia t ype 1 (MEN 1). This autosomal dominant syndrome is characterized by tu mours of the pancreas, parathyroid and pituitary. Inoperable carcinoid tumour is best treated with a long-acting somatostatin analogue, octr eotide. A diagnosis of MEN 1 has important connotations for the proban d's first-degree relatives, who should be entered into an appropriate screening programme.