MACRODACTYLY - REPORT OF 8 CASES OF A RARE ANOMALY

Citation
N. Kostakoglu et al., MACRODACTYLY - REPORT OF 8 CASES OF A RARE ANOMALY, Turkish Journal of Pediatrics, 38(1), 1996, pp. 73-79
Citations number
8
Categorie Soggetti
Pediatrics
ISSN journal
00414301
Volume
38
Issue
1
Year of publication
1996
Pages
73 - 79
Database
ISI
SICI code
0041-4301(1996)38:1<73:M-RO8C>2.0.ZU;2-W
Abstract
Macrodactyly or megalodactyly is a rare anomaly of the extremities. Ne ural factors are involved in the etiology. Presented here are eight ca ses which comprise five macrodactylous toes and three fingers. The mea n age at first referral was 6.8 years. Six patients underwent resectio n of the proximal phalanges together with bulk reduction of the soft t issue mass. Only soft tissue reduction was performed in the remaining two patients. Skin necrosis was observed in two cases, one of which ne cessitated amputation at the proximal interphalangeal joint level. The functional outcome was evaluated as poor with limited range of motion and stiffness in the joints. As far as functional results are concern ed, macrodactylous toes had a better prognosis than that of fingers.