LANGERHANS CELL HISTIOCYTOSIS ASSOCIATED WITH RECURRENT PNEUMOTHORAX - A CASE-REPORT

Pulmonary involvement of Langerhans cell histiocytosis (LCH) is an unc ommon but important cause of pulmonary fibrosis and honeycombing in yo ung adults. Rarely, pulmonary LCH may be complicated by spontaneous pn eumothorax. It may be isolated or associated with multiple organ invol vement. We describe here a case of LCH with diabetes insipidus, skin l esions and pulmonary involvement in a 15-year-old boy. The case was co mplicated by four episodes of spontaneous pneumothorax with typical ra diologic findings of pulmonary LCH. His presentation, radiologic findi ngs, treatment and clinical course during three-years of follow-up are discussed.