WILMS-TUMOR AND ASSOCIATED MALFORMATIONS - REPORT OF 2 CASES WITH WAGR AND DRASH SYNDROME

Authors
OZBEY H BONEVAL C KAPRAN Y AKSOYEK S SALMAN T CELIK A
Citation
H. Ozbey et al., WILMS-TUMOR AND ASSOCIATED MALFORMATIONS - REPORT OF 2 CASES WITH WAGR AND DRASH SYNDROME, European journal of pediatric surgery, 6(3), 1996, pp. 186-188
Citations number
15
Categorie Soggetti
Surgery,Pediatrics
Journal title
European journal of pediatric surgery → ACNP
ISSN journal
09397248
Volume
6
Issue
3
Year of publication
1996
Pages
186 - 188
Database
ISI
SICI code
0939-7248(1996)6:3<186:WAAM-R>2.0.ZU;2-T
Abstract
The combination of Wilms' tumor with aniridia, ambiguous genitalia/gon adoblastoma and mental retardation is defined as WAGR syndrome. The as sociation with pseudohermaphroditism and nephropathy was also describe d as Drash syndrome. Here we report two cases with WAGR and Drash synd rome. The importance of early recognition and appropriate management o f Wilms' tumor with those concurrent malformations is highlighted.